NUMERO: #20240969

Título: PIERRE ROBIN SEQUENCE: NARRATIVE LITERATURE REVIEW AND CASE REPORTS

Nome do Apresentador: Alana Lima Dos SANTOS

Categoria do Trabalho: Painel de Revisões narrativas ou sistemáticas (PRN)

Área Temática: Odontologia para pacientes especiais

Resumo: The Pierre Robin Sequence (PRS) is a rare congenital anomaly, defined by the clinical triad of micrognathia, glossoptosis and breathing difficulties. Therefore, this study aims to present the most common oral and craniofacial manifestations found in these patients. For this purpose, articles published since 2019 were accessed on Pubmed using the keywords "pierre robin sequence", "oral manifestations", "craniofacial manifestations". After a careful review, ten articles were chosen. In addition, we present two cases of patients treated at a reference center in northeastern Brazil, to illustrate the phenotypic diversity: one presenting PRS with cleft palate, and one presenting Stickler syndrome. The abnormalities associated with PRS are diverse: they can be isolated, associated with cleft palate and/or syndromes, or incompatible with life. Thus, health professionals should know this clinical condition. A multidisciplinary team must ensure its approach, diagnosis, and management to prevent irreversible sequelae.

Autor 1:  Alana Lima Dos SANTOS

E-mail 1:  [email protected]

Autor 2:   Liova Chabot Díaz

E-mail 2:  [email protected]

Autor 3 :  Mário Rogério Lima Mota

E-mail 3:  [email protected]

Autor 4:  Giovanna Teixeira Nunes

E-mail 4:  [email protected]

Autor 5:  José Ferreira da Cunha Filho

E-mail 5:  [email protected]