NUMERO: #20240769

Título: RAPIDLY GROWING PEDIATRIC RHABDOMYOSARCOMA: CLINICAL, TOMOGRAPHIC AND HISTOLOGICAL ASPECTS

Nome do Apresentador: Livian Isabel de Medeiros CARVALHO

Categoria do Trabalho: Painel de caso clínico (PCC)

Área Temática: Estomatologia

Resumo: An 8-year-old female exhibited swelling after a tooth extraction, prompted by severe mobility of deciduous teeth and a tissue mass. The extraoral examination displayed significant swelling on the right side of the face, causing noticeable asymmetry. An intraoral examination uncovered a lobulated, erythematous tumor-like lesion. Panoramic radiography showed a radiolucent area in the right maxillary region, indicating a "floating teeth" pattern and root resorption. Computed tomography revealed an ill-defined hypodense mass extending to the orbit, nasal fossa, and right maxillary sinus. An incisional biopsy identified a proliferation of atypical round and spindle cells within a variably myxoid or fibrous stroma. Immunohistochemistry tests for desmin, myogenin, and the MYOD1 gene were positive, confirming a diagnosis of rhabdomyosarcoma. Following the diagnosis, the patient underwent radiotherapy and chemotherapy. Eight months into treatment, there has been no recurrence of the lesion, and she remains under careful observation.

Autor 1:  Livian Isabel de Medeiros CARVALHO

E-mail 1:  [email protected]

Autor 2:   Eduarda Gomes Onofre DE ARAÚJO

E-mail 2:  [email protected]

Autor 3 :  Hélder Domiciano Dantas MARTINS

E-mail 3:  [email protected]

Autor 4:  Keila Martha Amorim BARROSO

E-mail 4:  [email protected]

Autor 5:  Amanda Maria Medeiros de Araújo LUCK

E-mail 5:  [email protected]

Autor 6:  Alexandre Rolim DE PAZ

E-mail 6:  [email protected]

Autor 7:  Paulo Rogério Ferreti BONAN

E-mail 7:  [email protected]