NUMERO: #20220255

Título: SYNCHRONOUS ODONTOGENIC MYXOMA AND ODONTOGENIC KERATOCYSTS IN NEVOID BASAL CELL CARCINOMA SYNDROME: A CASE REPORT

Nome do Apresentador: Roberto de Oliveira JABUR

Categoria do Trabalho: Trabalhos Aprovados para Disponibilização em Vídeo (ADV)

Área Temática: Estomatologia

Resumo: Nevoid basal cell carcinoma syndrome (NBCCS) is a hereditary condition characterized by a wide range of developmental abnormalities and a predisposition to neoplasms. An 11-year-old girl was referred for evaluation due to lack of eruption of teeth 14 and 15. Her past medical history and physical examination were unremarkable. Imaging exams showed well-defined pericoronal radiolucencies associated with teeth 14 and 37, as well as an additional radiolucent lesion affecting the right mandibular body. Microscopic analyses of both pericoronal lesions revealed to be odontogenic keratocysts (OKC). The additional mandibular lesion showed a proliferation of spindle and stellate cells in a predominantly myxoid stroma and numerous concentric basophilic calcifications, consistent with odontogenic myxoma (OM). The patient was referred for genetic counseling and the diagnosis of NBCCS was made. To the best of our knowledge, this represents the second case of synchronous OKC and OM in a patient with NBCCS

Autor 1:  Roberto de Oliveira JABUR

E-mail 1:  [email protected]

Autor 2:   Marcelo Carlos BORTOLUZZI

E-mail 2:  [email protected]

Autor 3 :  Ana Luiza Oliveira Corrêa ROZA

E-mail 3:  [email protected]

Autor 4:  Amanda Almeida LEITE

E-mail 4:  [email protected]

Autor 5:  Márcio Ajudarte LOPES

E-mail 5:  [email protected]

Autor 6:  Pablo Agustin VARGAS

E-mail 6:  [email protected]