NUMERO: #20250224

Título: PROGRESSIVE HEMIFACIAL ATROPHY IN A PEDIATRIC PATIENT: A CASE REPORT

Nome do Apresentador: Ilan Hudson Gomes de SANTANA

Categoria do Trabalho: Painel de caso clínico (PCC)

Área Temática: Cirurgia e traumatologia bucomaxilofacial

Resumo: Progressive hemifacial atrophy (PHA), also known as Parry-Romberg syndrome, is a rare condition of as yet undefined etiology, characterized by unilateral and progressive atrophy of the skin, subcutaneous fat, muscles and bones of the face. The incidence is estimated at 1 case per 700,000 individuals. We report the case of a 10-year-old male patient who sought dental care due to pain in the temporomandibular joint. Clinical examination revealed slight facial asymmetry, with mild soft tissue atrophy and skin thinning. Oroscopic examination revealed limited mouth opening and signs of muscle involvement. Radiographically, slight mandibular bone asymmetry was noted. Magnetic resonance imaging revealed a hyperintense lesion with a gliotic aspect in the right anterior nucleocapsular region, compatible with a perfusion disorder. Investigation for autoimmune diseases, including FAN, Anti-DNA, Anti-Scl 70, Anti-centromere and Anti-RNP, was negative, ruling out systemic collagenosis to date. The case reinforces the different approaches to diagnosing AHP.

Autor 1:  Ilan Hudson Gomes de SANTANA

E-mail 1:  [email protected]

Autor 2:   Carlos Eduardo de Oliveira Goes

E-mail 2:  [email protected]

Autor 3 :  Isabella Bezerra Araújo Cirilo

E-mail 3:  [email protected]

Autor 4:  Helder Domiciano Dantas Martins

E-mail 4:  [email protected]

Autor 5:  Karolayne Dutra Felix

E-mail 5:  [email protected]

Autor 6:  Maria Renata Caballero Lettieri Pinto

E-mail 6:  maria. [email protected]

Autor 7:  Paulo Rogério Ferreti Bonan

E-mail 7:  [email protected]